Angiomyolipoma with Epithelial Cysts
A Case Report and Review of Literature
DOI:
https://doi.org/10.21141/PJP.2026.613Keywords:
angiomyolipoma, angiomyolipoma with epithelial cysts, kidney neoplasms, histopathology, immunohistochemistry, case reportAbstract
Angiomyolipoma with epithelial cysts (AMLEC) is a rare subtype of angiomyolipoma that may closely mimic both malignant and benign neoplasms. We report a case of AMLEC in an 18-year-old female presenting with acute flank pain and radiologic suspicion for malignancy. This case highlights the diagnostic challenges posed by AMLEC, emphasizes its characteristic histopathologic and immunohistochemical features, and reviews current concepts regarding its pathogenesis. This case represents the first documented case of AMLEC in the Philippines.
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Copyright (c) 2026 Pia Nenita Duque, Jeffrey So, Jose Gabriel Gonzales, Josefino Castillo, Joseph Vincent Songco

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