Angiomyolipoma with Epithelial Cysts

A Case Report and Review of Literature

Authors

  • Pia Nenita Duque St. Luke’s Medical Center, Quezon City, Philippines https://orcid.org/0000-0002-4407-2108
  • Jeffrey So St. Luke’s Medical Center, Quezon City, Philippines
  • Jose Gabriel Gonzales St. Luke’s Medical Center, Quezon City, Philippines
  • Josefino Castillo St. Luke’s Medical Center, Quezon City, Philippines
  • Joseph Vincent Songco St. Luke’s Medical Center, Quezon City, Philippines https://orcid.org/0009-0001-1691-8241

DOI:

https://doi.org/10.21141/PJP.2026.613

Keywords:

angiomyolipoma, angiomyolipoma with epithelial cysts, kidney neoplasms, histopathology, immunohistochemistry, case report

Abstract

Angiomyolipoma with epithelial cysts (AMLEC) is a rare subtype of angiomyolipoma that may closely mimic both malignant and benign neoplasms. We report a case of AMLEC in an 18-year-old female presenting with acute flank pain and radiologic suspicion for malignancy. This case highlights the diagnostic challenges posed by AMLEC, emphasizes its characteristic histopathologic and immunohistochemical features, and reviews current concepts regarding its pathogenesis. This case represents the first documented case of AMLEC in the Philippines.

 

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Author Biographies

Pia Nenita Duque, St. Luke’s Medical Center, Quezon City, Philippines

Institute of Pathology, St. Luke’s Medical Center, Quezon City, Philippines

Jeffrey So, St. Luke’s Medical Center, Quezon City, Philippines

Institute of Pathology, St. Luke’s Medical Center, Quezon City, Philippines

Jose Gabriel Gonzales, St. Luke’s Medical Center, Quezon City, Philippines

Institute of Pathology, St. Luke’s Medical Center, Quezon City, Philippines

Josefino Castillo, St. Luke’s Medical Center, Quezon City, Philippines

Institute of Pathology, St. Luke’s Medical Center, Quezon City, Philippines

Joseph Vincent Songco, St. Luke’s Medical Center, Quezon City, Philippines

Institute of Pathology, St. Luke’s Medical Center, Quezon City, Philippines

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Published

06/11/2026

How to Cite

Duque, P. N., So, J., Gonzales, J. G., Castillo, J., & Songco, J. V. (2026). Angiomyolipoma with Epithelial Cysts: A Case Report and Review of Literature. The Philippine Journal of Pathology, 11(1). https://doi.org/10.21141/PJP.2026.613